Systemic Sclerosis
Cross-source consensus on Systemic Sclerosis from 1 sources and 5 claims.
1 sources · 5 claims
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Highlighted claims
- Systemic sclerosis is a rare autoimmune disorder characterised by progressive fibrosis of the skin and internal organs, causing increased tissue thickness and rigidity alongside vascular complications. — Effects of multimodal nutritional intervention on nutritional status and clinical outcomes in patients with systemic sclerosis: study protocol for a randomised controlled trial
- SSc has a combined prevalence of 17.6 per 100,000 person-years and an incidence of 1.4 per 100,000 person-years. — Effects of multimodal nutritional intervention on nutritional status and clinical outcomes in patients with systemic sclerosis: study protocol for a randomised controlled trial
- The standardised mortality ratio for SSc ranges from 2.82 to 3.4, with mortality risk particularly elevated in younger and male patients. — Effects of multimodal nutritional intervention on nutritional status and clinical outcomes in patients with systemic sclerosis: study protocol for a randomised controlled trial
- SSc clinical manifestations include Raynaud's phenomenon, gastrointestinal complications, inflammatory skin disease, swollen fingers, musculoskeletal inflammation, lung fibrosis, pulmonary arterial hypertension, and renal crisis. — Effects of multimodal nutritional intervention on nutritional status and clinical outcomes in patients with systemic sclerosis: study protocol for a randomised controlled trial
- Severe gastrointestinal involvement is the primary driver of malnutrition in SSc patients. — Effects of multimodal nutritional intervention on nutritional status and clinical outcomes in patients with systemic sclerosis: study protocol for a randomised controlled trial